Budd-Chiari综合征(附9例报告)

<正> Budd-Chiari综合征(B-CS)比较少见,但近年有增多趋势,常误诊为肝硬化等其他疾病,现结合我们所见9例报告、讨论如下: 资料来源为我院1962—1982年所见病例。9例中7例经下腔静脉导管和/或造影确诊;2例系临床诊断,其诊断根据是:有确切的门脉高压证据,同时又有明显的下腔静脉阻塞征象。

Budd-Chiari Syndrome—A Report of Nine Cases

Budd-Chiari syndrome is a rare disease and more often confused with hepatic cirrhosis. We report nine cases of the disease seen in our hospital in the past 20 years. The case number is the greatest among the case groups which have been reported in our country. The diagnosis was made by angiography (7 cases) and clinical. findings (2 cases). Among 9 cases, 7 were men and 2 women, (mean age, 28.7 years). On the basis of the data obtained from the 9 patients and our experience the clinical manifestations of the disease were classified into four kinds: 1) hepatic changes, as hepatomegaly, and hepatalgia (in the right upper abdomen or in the epigastrium); 2) symptoms of hyperten sion, such as ascites, esophageal varices, hematemesis and so on; 3) obstruction of inferior vena cava, resulting in phlebectasia in the lateral abdominal wall and Iegs, edema in the legs and the perineum, etc.; 4) cardiovascular symptoms, such as dyspnea, palpitation, cyanosis. The acute form of the disease was characterized by abdominal pain, nausea, vomiting, cardiovascular symptoms, progressive hepatic enlargement, rapid ascites formation, with a rare splenomegaly; the chronic form was characterized by coexistence of portal hypertension and obstruction of inferior vena eava. In addition, discussion was performed on the concept, etiology, diagnosis and differential diagnosis and treatment.